Congenital giant cerebriform melanocytic nevus

Abstract

Congenital melanocytic nevus is found in 1% to 2% of all newborn infants. Those measuring more than 20 cm are termed as giant variety. Cerebriform melanocytic nevus is one of the very rare form of giant variety (2, 3). Giant cerebriform melanocytic naevi over head and neck area can be associated with mental retardation, seizures and neurological manifestations and leptomeingeal melanosis. Superficial spreading malignant melanoma is the commonest malignancy seen in these nevi. It usually occurs after puberty and much earlier as compared to general population. The lifetime risk of developing melanoma in these patients ranges between 4.6% to 14% (2, 3). After treatment, aimed at improving the esthetic appearance and decrease the risk of malignancy, frequent monitoring and regular follow up is necessary (1).