Lethal prematurity ichthyosis syndrome in a newborn.

Abstract

Ichthyosis prematurity syndrome (IPS) is a rare condition characterized by prematurity, thickened epidermis, vernix caseosa-like scaling and neonatal asphyxia. A neonatal case of IPS was here reported. Despite all the attention aimed at dealing with respiratory distress, possible infections, dehydration and nutritional deficit, fatal sepsis could not be avoided.