Initial segmental cutaneous scleroderma/Unilateral nevoid telangiectasia.

Abstract

Localized cutaneous scleroderma is the most frequent connective tissue disease of childhood. Its lesions are often distributed along a cutaneous segment and are characterized by an initial inflammatory phase. The latter is followed by a characteristic hardening of the skin. In the well developed lesion a peripheral inflammatory ring often persists around the central sclerotic plaque.
Also unilateral nevoid telangiectasia is characterized by a segmental distribution. It is remiscent of port-wine stain, due both to its metameric distribution and color of the lesions. However, unilateral nevoid telangiectasia is acquired, often in the first decade of life, whereas port-wine stain is present since birth.